Παιδιατρική | Τόμος 63 • Τεύχος 5 • Σεπτέμβριος - Οκτώβριος 2000

SEPT-OCT.2000

30-05-03

14:03

™ÂÏ›‰·433

¶∞π¢π∞∆ƒπ∫∏ 2000;63:433-437

3. Robertson GL. Thirst and vasopressin function in normal and disordered states of water balance. J Lab Clin Med 1983;101:351-371.

4. Halter JB, Goldberg AP, Robertson GL, Porte D. Selective osmoreceptor dysfunction in the syndrome of chronic hypernatremia. J Clin Endocrinol Metab 1977;44:609-616.

5. Zerbe RL, Baylis PH, Robertson GL. Vasopressin function in clinical disorders of water balance. In: Robertson G, Beardwell CG, eds. Clinical endocrinology, vol 1. London: Butterworths; 1981. p. 297-329.

6. Schaff-Blass E, Robertson GL, Rosenfield RL. Chronic hypernatremia from a congenital defect in osmoregulation of thirst and vasopressin. J Pediatr 1983;102:703-708.

7. Radetti G, Rizza F, Mengarda G, Pittschieler K. Adipsic hypernatremia in two sisters. Am J Dis Child 1991;145: 321-325.

EӉȷʤÚÔ˘Û˜ ÂÚÈÙÒÛÂȘ

8. Robertson GL. The pathophysiology of ADH secretion. In: Tolis G, ed. Clinical neuroendocrinology: A pathophysiological approach. New York: Raven Press; 1979. p. 247-260.

9. Streeten DHP, Moses AM, Miller M. Disorders of the neurohypophysis. In: Braunwald E, Isselbacher KJ, Petersdorf RG, Wilson JD, Martin JB, Fauci AS, eds.

Harrison’s principles of internal medicine. 11th ed. New York: McGraw-Hill Book Company; 1987. p. 1722-1732.

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OÈ ¯·Ú·ÎÙËÚÈÛÙÈΤ˜ ‰ÂÚÌ·ÙÈΤ˜ Ù˘ ·ÏÏÔÈÒÛÂȘ, Ô˘ ÚÔÛÔÌÔÈ¿˙Ô˘Ó Ì «ÊÏÔÈfi ÔÚÙÔηÏÈÔ‡» (peau d’orange appearance), Û˘Ó‰˘¿˙ÔÓÙ·È Û ·ÚÎÂÙ¤˜ ÂÚÈÙÒÛÂȘ ÂÓËÏ›ÎˆÓ ·ÛıÂÓÒÓ ÌÂ Ù˘ÈΤ˜ ‰ÂÚÌ·ÙÈΤ˜ ‚Ï¿‚˜ ÌÔÚÊ·›·˜. ∏ ·ÈÙÈÔÏÔÁ›· Ù˘ ·Ú·Ì¤ÓÂÈ ¿ÁÓˆÛÙË. ∏ ‰È¿ÎÚÈÛ‹ Ù˘ ·fi ÙȘ ¿ÏϘ ÌÔÚʤ˜ ÂÓÙÔÈṲ̂ÓÔ˘ ÛÎÏËÚÔ‰¤ÚÌ·ÙÔ˜ Â›Ó·È ‰˘Û¯ÂÚ‹˜. ∞Ó·ÛÎÔÂ›Ù·È Ë ÎÏÈÓÈÎÔÂÚÁ·ÛÙËÚȷ΋ ÚÔ‚ÔÏ‹, Ë ıÂÚ·¢ÙÈ΋ ·ÓÙÈÌÂÙÒÈÛË Î·È Ë ÚfiÁÓˆÛË Ù˘ ÓfiÛÔ˘. ¶·È‰È·ÙÚÈ΋ 2000;63:433-437. §¤ÍÂȘ ÎÏÂȉȿ: ÛÎÏËÚfi‰ÂÚÌ·, ˈÛÈÓÔÊÈÏÈ΋ ÂÚÈÙÔÓÈ›Ùȉ·, ÌÔÚÊ·›·.

P. Zosi, H. Georgiadis, D. Karakaidos, D. Tsilivakos, T. Vlahou, C. Drakou, C. Karis. ∞ rare case of scleroderma in childhood. Case report. Paediatriki 2000;63:433-437. ● Abstract: We report a case of eosinophilic fasciitis (EF) associated with morphea in a 8.5 year old girl. EF is a type of scleroderma, rare in childhood, which is characterized by thickened, bound-down skin with cobblestone or peau d’orange appearance. EF and morphea commonly occur together, often in different locations. The distinction between EF and various forms of localized scleroderma remains unclear. The various types of the disease, their clinical presentation, treatment and prognosis are reviewed.

Key words: scleroderma, eosinophilic fasciitis, morphea.

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