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Rate of  Weight  Gain:   • Weight  gain  per  day  should  be  monitored  closely  at   each  visit   • Children  with  SMA  should  have  a  slower  weight   gain  velocity  than  a  healthy  child  of  the  same  age   • It  is  more  important  to  look  at  weight  trends  on  the   growth  chart  than  to  focus  on  specific  numbers     Weight  for  Length  or  BMI:     • Due  to  their  lower  amounts  of  lean  body  mass,   children  with  SMA  should  ideally  fall  somewhere   within  the  3rd  to  25th  percentile  on  the  growth  chart   for  BMI  or  weight  for  length     • However,  some  children  with  SMA  are  below  the   3rd  percentile  but  look  well-­‐nourished  on  exam   o Use  weight  for  length  until  24  months,  and   BMI  thereafter  

Length  or  Height:  

• It is  important  that  length-­‐for-­‐age  or  height-­‐for-­‐age   does  not  fall  below  the  3rd  percentile;  falling  below   this  threshold  may  indicate  suboptimal  nutritional   status   • Length  or  height  may  be  difficult  to  measure  in   children  with  SMA  using  standard  methods.  Arm   span,  arm  length,  or  tibia  length  may  be  used  to   approximate  length  or  height3  

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Nutritional Management of Children with SMA: A Toolkit  
Nutritional Management of Children with SMA: A Toolkit  
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