986
YEE
Fig. 2. ECG of TAPVR with right atrial enlargement, right ventricular hypertrophy.
Tricuspid atresia Tricsupid atresia represents 1% to 2% of congenital heart disease in infancy [16]. There is no tricuspid valve and there is underdevelopment of the right ventricle and pulmonary artery. Therefore, pulmonary blood ow is decreased. With no ow across the right atrium to the right ventricle, the right atrium needs a right-to-left shunt to empty, making an ASD, VSD, or PDA essential for survival. The great arteries are transposed in 30% of the cases, with a VSD and no pulmonic stenosis. In 50% of cases there is normal artery anatomy, with a small VSD and pulmonic stenosis.
Fig. 3. Chest radiograph of TAPVR with cardiomegaly and increased vascular markings.